Revue de Pneumologie Clinique – Vol. 69 – N° 1 – p. – La maladie de Castleman: observations inhabituelles et revue de la littérature – EM|consulte. Disease definition. Castleman disease (CD) is a benign lymphoproliferative disorder that may present as a localized or multicentric form (see these terms). Introduction La maladie de Castleman (MC) est une affection rare, caractérisée par l’existence d’une forme localisée et d’une forme.

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Orphanet: Maladie de Castleman

The second one is characterized by an uncommon radiological presentation, with a calcification within the tumor. A report of two cases and a review of the literature. Nous rapportons trois observations de maladie de Castleman unicentrique. N Engl J Med La maladie de Castleman: Castleman disease CD is a benign lymphoproliferative disorder, rare in children.

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Identification of two homologs of the Kaposi’s sarcoma-associated herpesvirus human herpesvirus 8 in retroperitoneal fibromatosis of different macaque species. Cas cliniques Observation 1. You may thus request that your data, should it be inaccurate, incomplete, unclear, outdated, not be used or stored, be corrected, clarified, updated or deleted. Access to the full text of this article requires a subscription.


Journal page Archives Contents list. Access to the PDF text. Cervical Castleman disease in childhood: Induction of B cell hyperplasia in simian immunodeficiency virus-infected rhesus macaques with the simian homologue of Kaposi’s sarcoma-associated herpesvirus.

While surgery is the treatment for maladje lesions, steroids and chemotherapy are indicated in the multicentric type. Human herpesvirus 8 encodes a homolog of interleukin Akkad dB. Health care resources casgleman this disease Expert centres Diagnostic tests 8 Patient organisations 36 Orphan drug s 4.

You can move this window by clicking on the headline. Multicentric Castleman’s disease in HIV infection: Other search option s Castlemxn list. You can move this window by clicking on the headline.

Remy-Jardin bfA. Angiogenesis and hematopoiesis induced by Kaposi’s sarcoma-associated herpesvirus-encoded interleukin Molecular mimicry of human cytokine and cytokine response pathway genes by KSHV.

Journal Tunisien d’ORL et de Chirurgie Cervico-Faciale

Human herpesvirus type 8 interleukin-6 homologue is functionally active on human myeloma cells. They underlie the difficulty of surgical resection due to the tumor vascularization.

HHV-8 is associated with plasmablastic variant of Castleman’s disease that is linked to HHV-8 positive plasmablastic lymphoma. Only comments written in English can be processed. As per the Law relating to information storage and personal integrity, you have the right to oppose art 26 of that lawaccess art 34 of that law and rectify art 36 of that law your personal data.


The pathological features and the therapeutic management of CD are discussed. Journal page Archives Contents list. Additional information Further information on this disease Classification s 2 Gene s 0 Other website s 6. The clinical manifestations are heterogeneous, ranging from asymptomatic discrete lymphadenopathy to recurrent caetleman of diffuse lymphadenopathy with severe systemic symptoms. Personal information regarding our website’s visitors, including their identity, is confidential.

Castleman disease is a rare disorder of caetleman lymphoid system which can be classified into two clinical groups, monocentric disease versus multicentric disease, and two histological types, the hyaline vascular form versus the plasma cell form.

The documents contained in this web site are presented for information purposes only. Both young patients were affected with an isolated neck localization of Castleman disease. Exacerbations of clinical symptoms in human immunodeficiency virus type 1-infected patients with multicentric Castleman’s disease are associated with a high increase in Castlemwn sarcoma herpesvirus DNA load in peripheral blood mononuclear cells.

Two forms have been described: